Epidemiology

• First described in 1964

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Etiology

• xxx

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Physiology

• xx

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Diagnosis

• xx

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Clinical Presentation

• Yellow Discoloration of Fingernails:
• Lymphedema:
• Pleural Effusion (see [[Pleural Effusion-Exudate]]): present in some cases
• Bronchiectasis (see [[Bronchiectasis]]): present in some cases
  • Due to hypoplasia of lymphatics (with altered lung drainage) or immunologic deficiencies (that are present in some cases)
  • Of the original 12 cases, 3/5 with documented bronchiectasis also had chronic sinusitis (suggesting mucociliary dysfunction)

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Treatment

• xx

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References

• xx