Combined Pulmonary Fibrosis and Emphysema

Epidemiology

  • xxx

Clinical

  • Pulmonary Fibrosis (lower zone-predominant) + Emphysema (upper zone-predominant) (see ILD-Etiology, [[ILD-Etiology]] and Obstructive Lung Disease, [[Obstructive Lung Disease]]):
  • Pulmonary Hypertension (see Pulmonary Hypertension, [[Pulmonary Hypertension]]): occurs in almost 50% of cases

References

  • Cottin V, Nunes H, Brillet PY, et al. Combined pulmonary fibrosis and emphysema: a distinct underrecognised entity. Eur Respir J 2005;26:586-93