Congenital Long QT Syndrome

Epidemiology

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Etiology

  • Jervell and Lange-Neilsen Syndrome
    • Epidemiology: less common type
    • Inheritance: autosomal recessive
    • Clinical: sensorineural deafness + prolonged QT
    • Prognosis: more malignant clinical course
  • Romano-Ward Syndrome
    • Epidemiology: more common type
    • Inheritance: autosomal dominant
    • Clinical: purely cardiac phenotype (prolonged QT only)
  • Idiopathic Congenital Long QT Syndrome

Physiology

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Diagnosis

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Clinical Manifestations

Cardiovascular Manifestations

Other Manifestations

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Treatment

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References

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